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Resumen. COLLAZO ALVAREZ, Hiralio; TORRECILLA SILVERIO, Dewar; MORALES FLORAT, Jorge Luis y COLLAZO MARIN, Stephens Yecc. Malignant. CASO CLÍNICO. Malignant oropharyngeal fibrous histiocytoma. Resection and radial reconstruction with fasciocutaneous flap. Histiocitoma fibroso maligno de. LETTERS TO THE EDITOR. Malignant fibrous histiocytoma – a rare hepatic tumor . Histiocitoma fibroso maligno, un tumor hepático raro.

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Malignant oropharyngeal fibrous histiocytoma.

J Laryngol Otol ; The most common sites of involvement include lower extremities mainly thigh followed by upper arms, retroperitoneum, viscera, head and neck in childhood. An incisional biopsy revealed a fusocellular neoplasm constituted by a population of fibrohistiocytic cells with a storiform growth pattern, which was compatible with malignant fibrohistiocytoma Fig. Ann Otolaryngol Chir Cervicofac ; Radiation-induced malignant fibrous histiocytoma of the neck in a patient with laryngeal carcinoma.

Malignant fibrous histiocytoma is recognized as the most common soft-tissue sarcoma in adults, although its location in the pharynx is unusual. Abdomen was soft but volumous with positive ascitic wave, tenderness in the right hypocondrium but no distinct hepatomegaly was found.

The etiology of the tumor remains unknown. Anorexia, malaise, fever and weight loss are present in retroperitoneal and inflammatory forms of UPS. In conclusion, although of rare occurence, MFH should be considered in the differential diagnosis of large liver lesions. Previous irradiation was not found in our case. Inadequate resection is related to a higher local recurrence rate and worse prognosis.


They were arrayed forming imbricated bundles and adopting a storiform growth pattern in areas, which confirmed the initial diagnosis.

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Malignant fibrous histiocytoma – a rare hepatic tumor. In the myxoid variant, mesenchymal cells are present in a myxoid stroma rich in mucopolysaccharides. Chemotherapy CHT with ifosfamide, trabectedin, dacarbazine, pazopanib have demonstrated efficacy in UPS and ma,igno registered and available in most European Union countries.

Only comments written in English can be processed. Clinical case We present a case of a yr-old-man was admitted to our hospital because of abdominal distension causing discomfort, lower extremities edema and weight loss.

Orphanet: Histiocitoma fibroso maligno

June Pages Discussion Since the first report of MFH in maligjo O’Brien and Stout, it has been well recognized as the most common malignant vibroso tissue tumor. For all other comments, please send your remarks via contact us. Intraabdominal and retroperitoneal cases may be accompanied by constitutional syndrome, but at other sites it is not a habitual clinical manifestation.

Most cases previously diagnosed as malignant fibrous histiocytoma have been reclassified into other histological types of sarcoma. Therefore, no consensus exists yet on the indication for administering treatment complementary to surgery in MFH.

Myxoid malignant fibrous histiocytoma of the uterus, a case with immunohistochemical, fibrodo a tumor cell culture studies. Since the first report of MFH in by O’Brien and Stout, it has been well recognized as the most common malignant soft tissue tumor.


No remarkable abnormalities in laboratory findings. In case of tumors in which adequate margins are not possible due to their location or large size, postoperative irradiation may improve control of the disease.

Histiocitoma fibroso maligno

How to cite this article. Resection and radial reconstruction with fasciocutaneous flap Histiocitoma fibroso maligno de orofaringe. Ochandiano Caicoya 2J.

Hepatic soft tissue sarcoma. Primary malignant fibrous histiocytoma of the mandible: It is classified, based on appearance and predominant cell population, into different subtypes: Mevio E, Sbrocca M, Malignant fibrous histiocytoma of the pharynx. Clinical description The tumor arises most commonly during the sixth and seventh decades of life. No pathological lymph node enlargement was observed. Visceral locations are uncommon and primary hepatic MFH is exceedingly rare.

J Oral Pathol ; The documents contained in this web site are fibrosi for information purposes only. The myxoid variant also exhibits a certain degree of cellular pleomorphism, but much less than the previous subtype.

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